Question
Biochemistry Question on Amino Acids
An infant is brought by his parents with complaints that his urine turns black on standing. Which of the following metabolic disorders is likely?
A
Phenylketonuria
B
Alkaptonuria
C
Homocystinuria
D
Maple syrup urine disease
Answer
Alkaptonuria
Explanation
Solution
The correct option is (B) : Alkaptonuria